منابع مشابه
Hematologic Studies on Erythropoietic Porphyria
With the technical assistance of Vicki Keefer E RYTHROPOIETIC porphyria is a rare inborn error of porphyrin metabolism; forty-two well documented cases have been described to date. Among the features common to this disorder is a hemolytic component of varying degree and severity. The precise nature of the hemolytic defect and its relationship to changes in other organs such as the liver and the...
متن کاملHematologic Studies on Erythropoietic Porphyria : A
With the technical assistance of Vicki Keefer E RYTHROPOIETIC porphyria is a rare inborn error of porphyrin metabolism; forty-two well documented cases have been described to date. Among the features common to this disorder is a hemolytic component of varying degree and severity. The precise nature of the hemolytic defect and its relationship to changes in other organs such as the liver and the...
متن کاملHEMATOLOGIC STUDiES ON ERYTHROPOIETIC PORPHYRIA 763
With the technical assistance of Vicki Keefer E RYTHROPOIETIC porphyria is a rare inborn error of porphyrin metabolism; forty-two well documented cases have been described to date. Among the features common to this disorder is a hemolytic component of varying degree and severity. The precise nature of the hemolytic defect and its relationship to changes in other organs such as the liver and the...
متن کاملStudies in Porphyria
A variety of 5beta steroid metabolites derived from hormones natural to man are potent inducers experimentally of delta-aminolevulinate synthetase, the rate-limiting enzyme in porphyrin-heme formation. This mitochondrial enzyme is found at high levels of activity in the livers of patients with the genetic disease, acute intermittent porphyria (AIP). In this study the metabolism of (14)C-labeled...
متن کاملExperimental hepatic porphyria caused by feeding 3,5-diethoxycarbonyl-1,4-dihydro-2,4,6-trimethylpyridine. Comparison with sedormid porphyria.
Since Schmid & Schwartz (1952) described an experimental hepatic porphyria induced in rabbits by Sedormid (2-isopropylpent-4-enoylurea), several drugs chemically related to Sedormid (Goldberg & Rimington, 1955; Stich & Decker, 1955a, b; Talman, Labbe & Aldrich, 1957) and some barbiturates (Goldberg, 1954a) have been shown to cause excretion of both porphobilinogen and porphyrins in animals. Gol...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: Nihon Naika Gakkai Zasshi
سال: 1964
ISSN: 0021-5384,1883-2083
DOI: 10.2169/naika.52.1189